Macrophage Activation Syndrome.
نویسندگان
چکیده
Macrophage Activation Syndrome (MAS) occurs as a severe life-threatening complication of several chronic rheumatic diseases. It is more frequent with systemic onset juvenile arthritis and adult onset Still's disease.1 It can be primary, infection related, malignancy associated or autoimmune3. We report a case of Macrophage Activation Syndrome presenting as pyrexia of unknown origin (PUO) and pancytopenia in the absence of any known triggering factor.
منابع مشابه
Macrophage Activation Syndrome as the First Impression of Kawasaki Disease; A Case Report
Introduction Macrophage activation syndrome (MAS) is a rare and life-threatening complication of Kawasaki Disease (KD) that is usually diagnosed at the same time or after KD. We report a case of MAS as the initial manifestation of KD. Case Report A previously healthy 3-year old girl was admitted to the pediatric infectious di...
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Macrophage activation syndrome (MAS) is a rare feature of rheumatic disorders in children and adolescence and its presentation as the first symptom of rheumatic disorders is very infrequent. A 9-year-old girl, in whom MAS developed, was admitted to our Hospital in Tehran, Iran. She suffered from high grade fever and rash followed by multiple joint swelling months afterwards. Bone marrow aspira...
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BACKGROUND Macrophage activation syndrome is a rare and life threatening complication of childhood rheumatic disorders. CASE CHARACTERISTICS 6-year-old male child with macrophage activation syndrome complicating systemic onset juvenile idiopathic arthritis. OBSERVATION He developed pericardial effusion, hyponatremia and deranged renal function. OUTCOME Improvement on intravenous cortico s...
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Macrophage activation syndrome is a rare and potentially life-threatening disease. It occurs due to immune dysregulation manifested as excessive macrophage proliferation, typically causing hepatosplenomegaly, pancytopenia and hepatic dysfunction. Here, we report an unusual case of macrophage activation syndrome presenting as dyspnea, as well as (reported here for the first time) high resolution...
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عنوان ژورنال:
- The Journal of the Association of Physicians of India
دوره 65 5 شماره
صفحات -
تاریخ انتشار 2017